ELISA SGSH anti-

Quantity:100µg Purification:Immunogen affinity purified Form:liquid Purity:?95% as determined by SDS-PAGE Host:Rabbit Clonality:polyclonal Clone ID: Isotype:IgG Storage:PBS with 0.02% sodium azide and 50% glycerol pH 7.3 , -20? for 12 months (Avoid repeated freeze / thaw cycles.) Background:This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sµLfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which resµLts from impaired degradation of heparan sµLfate. Transcripts of varying Quantitys have been reported but their biological validity has not been determined. Immunogen:N-sµLfoglucosamine sµLfohydrolase Synonyms:HSS Observed MW:57 kDa Uniprot ID:P51688 Reactivity:, Mouse, Rat Tested Application:ELISA, WB, IHC Recommended dilution:WB: 1:500 - 1:2000; IHC: 1:50 - 1:100 Gene ID:6448 Research Area:Metabolism