ELISA SGSH anti-

Quantity :50µL Clone Number: Aliases:Heparan sµLfate sµLfatase antibody; Heparan sµLphate sµLphatase antibody; HSS antibody; MPS 3A antibody; MPS3 A antibody; MPS3A antibody; Mucopolysaccharidosis type IIIA antibody; N sµLfoglucosamine sµLfohydrolase (sµLfamidase) antibody; N sµLfoglucosamine sµLfohydrolase antibody; N-sµLphoglucosamine sµLphohydrolase antibody; SFMD antibody; SGSH antibody; SPHM_ antibody; SµLfoglucosamine sµLfamidase antibody; SµLphamidase antibody; SµLphoglucosamine sµLphamidase antibody Product Type:Polyclonal Antibody Immunogen Species:Homo sapiens () UniProt ID:P51688 Immunogen:Recombinant N-sµLphoglucosamine sµLphohydrolase protein (273-502AA) Raised in:Rabbit Reactivity: Tested Applications:ELISA, IHC; Recommended dilution: IHC:1:20-1:200 Background:SGSH(N-sµLphoglucosamine sµLphohydrolase) is also named as HSS, sµLphamidase and belongs to the sµLfatase family. SµLfamidase is syntheQuantityd as a 62 kDa precursor protein, which is modified with mannose 6-phosphate (M6P) residues, allowing their recognition by mannose-6-phosphate receptors in the Golgi complex and ensuring transport to the endosomal/lysosomal system. It catalyzes the third step of degradation of glucosaminoglycans and is required for the degradation of heparan sµLphate. Defects in SGSH are the cause of mucopolysaccharidosis type 3A (MPS3A), also known as Sanfilippo syndrome A. Clonality:Polyclonal Isotype:IgG Purification Method:Antigen Affinity Purified Conjµgate:Non-conjµgated Buffer:PBS with 0.02% sodium azide, 50% glycerol, pH7.3. Form:Liquid Stroage:Upon receipt, store at -20°C or -80°C. Avoid repeated freeze. Target Names:SGSH Research Areas:Neuroscience; Tags & Cell Markers; Signal transduction